DIDŽIOJI BETA TALASEMIJA
Vaisiaus hemoglobino sintezės farmakologinė indukcija
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Vaisiaus hemoglobino sintezės farmakologinė indukcija
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Didžioji beta talasemija

Vaisiaus hemoglobino sintezės farmakologinė indukcija

Hidroksiurėjos (hidroksikarbamido) terapija

Efficacy of hydroxyurea in providing transfusion independence in β-thalassemia. (atsiveria naujas langas)

Ansari SH, Shamsi TS, Ashraf M, Perveen K, Farzana T, Bohray M, Erum S, Mehboob T.

Šaltinis‎: J Pediatr Hematol Oncol 2011;33(5):339-43.

Kodas‎: PubMed 21602718

DOI‎: 10.1097/MPH.0b013e31821b0770

https://www.ncbi.nlm.nih.gov/pubmed/21602718 (atsiveria naujas langas)

Decreased transfusion needs associated with hydroxyurea therapy in Algerian patients with thalassemia major or intermedia. (atsiveria naujas langas)

Bradai M, Pissard S, Abad MT, Dechartres A, Ribeil JA, Landais P, de Montalembert M.

Šaltinis‎: Transfusion 2007;47(10):1830-6.

Kodas‎: PubMed 17880608

DOI‎: 10.1111/j.1537-2995.2007.01399.x

https://www.ncbi.nlm.nih.gov/pubmed/17880608 (atsiveria naujas langas)

Hydroxyurea increases hemoglobin F levels and improves the effectiveness of erythropoiesis in beta-thalassemia/hemoglobin E disease. (atsiveria naujas langas)

Fucharoen S, Siritanaratkul N, Winichagoon P, Chowthaworn J, Siriboon W, Muangsup W, Chaicharoen S, Poolsup N, Chindavijak B, Pootrakul P, Piankijagum A, Schechter AN, Rodgers GP.

Šaltinis‎: Blood 1996;87(3):887-92.

Kodas‎: PubMed 8562958

https://www.ncbi.nlm.nih.gov/pubmed/8562958 (atsiveria naujas langas)

Genotype-phenotype relationship of patients with β-thalassemia taking hydroxyurea: a 13-year experience in Iran. (atsiveria naujas langas)

Karimi M, Haghpanah S, Farhadi A, Yavarian M.

Šaltinis‎: Int J Hematol 2012;95(1):51-6.

Kodas‎: PubMed 22180324

DOI‎: 10.1007/s12185-011-0985-6

https://www.ncbi.nlm.nih.gov/pubmed/22180324 (atsiveria naujas langas)

Clinical experience with fetal hemoglobin induction therapy in patients with β-thalassemia. (atsiveria naujas langas)

Musallam KM, Taher AT, Cappellini MD, Sankaran VG.

Šaltinis‎: Blood 2013;121(12):2199-212.

Kodas‎: PubMed 23315167

DOI‎: 10.1182/blood-2012-10-408021

https://www.ncbi.nlm.nih.gov/pubmed/23315167 (atsiveria naujas langas)

A randomised double-blind placebo-controlled clinical trial of oral hydroxyurea for transfusion-dependent β-thalassaemia. (atsiveria naujas langas)

Yasara N, Wickramarathne N, Mettananda C, Silva I, Hameed N, Attanayaka K, Rodrigo R, Wickramasinghe N, Perera L, Manamperi A, Premawardhena A, Mettananda S

Šaltinis‎: Sci Rep. 2022;12(1):2752.

Kodas‎: PubMed 35177777

DOI‎: 10.1038/s41598-022-06774-8

https://pubmed.ncbi.nlm.nih.gov/35177777/ (atsiveria naujas langas)

Response to hydroxyurea treatment in Iranian transfusion-dependent beta-thalassemia patients. (atsiveria naujas langas)

Yavarian M, Karimi M, Bakker E, Harteveld CL, Giordano PC.

Šaltinis‎: Haematologica 2004;89(10):1172-8.

Kodas‎: PubMed 15477200

https://www.ncbi.nlm.nih.gov/pubmed/15477200 (atsiveria naujas langas)

Hydroxyurea therapy in 49 patients with major beta-thalassemia. (atsiveria naujas langas)

Zamani F, Shakeri R, Eslami SM, Razavi SM, Basi A.

Šaltinis‎: Arch Iran Med 2009;12(3):295-7.

Kodas‎: PubMed 19400608

https://www.ncbi.nlm.nih.gov/pubmed/19400608 (atsiveria naujas langas)

Rekombinantinis eritropoetinas (vienas arba kartu su kitais preparatais)

Induction of fetal hemoglobin synthesis with recombinant human erythropoietin in anemic patients with heterozygous beta-thalassemia during pregnancy. (atsiveria naujas langas)

Breymann C, Fibach E, Visca E, Huettner C, Huch A, Huch R.

Šaltinis‎: J Matern Fetal Med 1999;8(1):1-7.

Kodas‎: PubMed 10052837

DOI‎: 10.1002/(SICI)1520-6661(199901/02)8:1<1::AID-MFM1>3.0.CO;2-O

https://www.ncbi.nlm.nih.gov/pubmed/10052837 (atsiveria naujas langas)

Treatment of beta-thalassemia patients with recombinant human erythropoietin: effect on transfusion requirements and soluble adhesion molecules. (atsiveria naujas langas)

Chaidos A, Makis A, Hatzimichael E, Tsiara S, Gouva M, Tzouvara E, Bourantas KL.

Šaltinis‎: Acta Haematol 2004;111(4):189-95.

Kodas‎: PubMed 15153710

DOI‎: 10.1159/000077551

https://www.ncbi.nlm.nih.gov/pubmed/15153710 (atsiveria naujas langas)

Fetal globin induction--can it cure beta thalassemia? (atsiveria naujas langas)

Perrine SP.

Šaltinis‎: Hematology Am Soc Hematol Educ Program 2005:38-44.

Kodas‎: PubMed 16304357

DOI‎: 10.1182/asheducation-2005.1.38

https://www.ncbi.nlm.nih.gov/pubmed/16304357 (atsiveria naujas langas)